AI Article Synopsis

  • Antineutrophil cytoplasmic antibody-related vasculitis (AAV) is a group of diseases that cause severe inflammation of small blood vessels, with subtypes including eosinophilic GPA, Microscopic Polyangiitis, and Granulomatosis with Polyangiitis.
  • A case report describes a 68-year-old man with AAV who experienced tingling and numbness in his legs, without respiratory symptoms or other organ involvement, confirmed by a nerve biopsy showing signs of vasculitic neuropathy.
  • After treatment with glucocorticoids and cyclophosphamide for six cycles, the patient's symptoms improved significantly, enhancing his quality of life.

Article Abstract

Antineutrophil cytoplasmic antibody-related vasculitis (AAV), is a group of diseases marked by systemic symptoms and severe small vessel inflammation. The three subtypes of AAV are eosinophilic GPA (EGPA), Microscopic Polyangiitis (MPA), and Granulomatosis with Polyangiitis (GPA). The organs that get involved in the disease process are the kidneys and the upper and lower respiratory tracts, with a spectrum of neurological manifestations. Here, we present a case report of a 68-year-old man who came with complaints of tingling and numbness over bilateral lower limbs for two months accompanied by difficulty in walking and bilateral foot drop without any respiratory complaints or involvement of sensory or autonomic system who was diagnosed with AAV (c-ANCA +) on further workup. A sural Nerve biopsy was done for confirmation which was suggestive of chronic, asymmetrical axonal neuropathy with perivascular inflammation, suggestive of vasculitic neuropathy. The patient had no other organ involvement. The patient was started on glucocorticoids and cyclophosphamide therapy for 6 cycles after which his symptoms and quality of life improved drastically.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC11050731PMC
http://dx.doi.org/10.7759/cureus.57046DOI Listing

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