AI Article Synopsis
- Left ventricular arrhythmogenic cardiomyopathy (ALVC) is a rare heart condition that has been reclassified as a type of non-dilated cardiomyopathy, and the review highlights its background, diagnosis, and risks of sudden cardiac death.
- There is limited data on ALVC, but it is recognized as a specific disease affecting the left ventricle, necessitating updated management strategies and understanding of associated risks.
- Diagnosis involves a comprehensive approach using cardiac magnetic resonance imaging and genetic testing, which are crucial for assessing the risk of sudden cardiac death and improving patient management, with more research needed to enhance knowledge about the condition.
Article Abstract
Purpose Of Review: Left ventricular arrhythmogenic cardiomyopathy (ALVC) is a rare and poorly characterized cardiomyopathy that has recently been reclassified in the group of non-dilated left ventricular cardiomyopathies. This review aims to summarize the background, diagnosis, and sudden cardiac death risk in patients presenting this cardiomyopathy.
Recent Findings: Although there is currently a lack of data on this condition, arrhythmogenic left ventricular dysplasia can be considered a specific disease of the left ventricle (LV). We have collected the latest evidence about the management and the risks associated with this cardiomyopathy.
Summary: Left ventricular arrhythmogenic cardiomyopathy is still poorly characterized. ALVC is characterized by fibrofatty replacement in the left ventricular myocardium, with variable phenotypic expression. Diagnosis is based on a multiparametric approach, including cardiac magnetic resonance (CMR) and genetic testing, and is important for sudden cardiac death (SCD) risk stratification and management. Recent guidelines have improved the management of left ventricular arrhythmogenic cardiomyopathy. Further studies are necessary to improve knowledge of this cardiomyopathy.
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| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC11012337 | PMC |
| http://dx.doi.org/10.3390/jcm13071835 | DOI Listing |
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