Heart Transplantation for Uhl Anomaly in an Adult.

JACC Case Rep

Division of Cardiovascular Surgery, Department of Surgery, Hospital of the University of Pennsylvania, University of Pennsylvania, Philadelphia, Pennsylvania, USA.

Published: May 2024

Uhl anomaly is characterized by the morphologic absence of right ventricular myocardium and is an exceedingly rare cause of nonischemic cardiomyopathy. We report the first case of a successful heart transplantation in a 41-year-old patient who presented in cardiogenic shock from Uhl anomaly causing decompensated right ventricular failure.

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Source
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC11002861PMC
http://dx.doi.org/10.1016/j.jaccas.2024.102322DOI Listing

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