Solid Pseudo-papillary Neoplasia: A Rare Malignancy of the Pancreas.

J Community Hosp Intern Med Perspect

Medstar Health Internal Medicine Residency Training Program, Baltimore, MD, USA.

Published: November 2023

Solid pseudopapillary neoplasms (SPNs) are exceedingly rare type of exocrine pancreatic malignancy, representing only 0.9%-2.7% of all exocrine pancreatic malignancies. They predominantly affect young women and unlike other pancreatic malignancies, they have excellent prognoses with 5-year survival following surgical resection approaching 97%. Given the rarity of the disease, little is known about their histopathogenesis as they do not harbor similar genetic mutational abnormalities like other pancreatic tumors. We describe a rare case of SPN in a young female who was found to have the rare diagnosis during the work up for deranged liver function tests.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC11000833PMC
http://dx.doi.org/10.55729/2000-9666.1254DOI Listing

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