Pierre Marie and Sainton syndrome, or cleido-cranial dysostosis is characterised by a triad: clavicular aplasia, delayed ossification of the fontanelles and sutures of the vault of the skull and hereditary transmission. To these may be added multiple dental inclusions - hence its interest in stomatology. The authors described a familial hereditary case affecting mother and son, the former with an incomplete syndrome and the latter with the complete picture of major dysostosis.
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