Low-grade fibromyxoid tumor of the dura: A new entity?

Surg Neurol Int

Department of Pathology, Children's Hospital of Los Angeles, University of Rochester School of Medicine, Rochester, United States.

Published: January 2024

Background: Low-grade fibromyxoid tumors are uncommon in children. Their differentiation from high-grade fibromyxoid tumors, as seen in adults, is imperative to diagnosis. Awareness of the entity and its subsequent behavior may guide management and predict outcomes.

Case Description: We describe the case of a previously unreported low-grade fibromyxoid tumor of the cerebellum in an 8-year-old male. Extensive immunohistochemical, next-generation sequencing, and attempted DNA methylation profiling are reported. There has been no recurrence during the 6-year follow-up. Screening excluded multiple myxoid tumors, including low-grade fibromyxoid sarcoma. The findings suggest that, with gross total resection, the lesions may not recur.

Conclusion: The case of fibromyxoid tumor with 6-year follow-up and the limited literature of similar tumors are reviewed.

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Source
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC10858751PMC
http://dx.doi.org/10.25259/SNI_830_2023DOI Listing

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