We present a case of primary rhabdoid tumour of the orbit. Presenting features at birth included congenital ptosis, conjunctival injection, hyphaema and microphthalmia. The unique presentation caused a late diagnosis following the development of rapid proptosis 6 months later. We suggest that orbital rhabdoid tumour be considered in the differential diagnoses of patients presenting with atypical persistent foetal vasculature features.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC10806956PMC
http://dx.doi.org/10.1136/bcr-2022-250776DOI Listing

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