Cellular angiofibroma is a rare benign mesenchymal tumor reported in genital region in middle-aged patients. We report a rare presentation of the tumor in an extragenital location-the arm of a young male patient. After biopsy, an en bloc excision of the mass was done and diagnosis was confirmed. No adjuvant treatment was required. Our patient had an unusual location for this rare tumor at an age younger than reported in literature so far. Imaging can only predict the mesenchymal nature of the tumor but histopathology and immunohistochemistry (IHC) is the cornerstone of diagnosis. Cellular angiofibroma has a good prognosis. Histopathology and IHC are needed to confirm the diagnosis, hence emphasizing the role of a good and experienced pathologist. The pathogenesis of the cellular angiofibroma is still not fully determined and current hormonal and immunotherapy suppression regimes will need further evaluation.
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