A case of erythromelalgia with gastrointestinal dysautonomia treated with immunoglobulin: A case report.

SAGE Open Med Case Rep

Dalla Lana School of Public Health & Division of Dermatology, Department of Medicine, University of Toronto, Toronto, ON, Canada.

Published: November 2023

AI Article Synopsis

  • An 18-year-old girl with a medical history of skin allergies, excessive sweating, and inflammation in her esophagus was diagnosed with two conditions: erythromelalgia (a painful skin condition) and gastrointestinal dysautonomia (problems with automatic bodily functions).
  • These issues were believed to be caused by autoimmune small fiber neuropathy (a nerve condition).
  • After starting treatment with intravenous immunoglobulin, she showed major improvements, suggesting her health problems were linked to an autoimmune disorder.

Article Abstract

An 18-year-old female with a history of atopic march, hyperhidrosis, and eosinophilic esophagitis was diagnosed with erythromelalgia and gastrointestinal dysautonomia secondary to presumed autoimmune small fiber neuropathy. The patient experienced significant clinical improvements after the initiation of intravenous immunoglobulin therapy, supporting an underlying autoimmune disorder.

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Source
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC10658769PMC
http://dx.doi.org/10.1177/2050313X231213137DOI Listing

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