Median mandibular cleft in SAMS syndrome - A rare case report.

Indian J Dent Res

Department of Obstetrics and Gynecology, Sree Balaji Medical College & Hospital, Chennai, Tamil Nadu, India.

Published: November 2023

Rationale: SAMS syndrome is a rare genetic disorder characterized by midline facial clefting, skeletal anomalies, and other defects.

Salient Features: Among the craniofacial manifestations of SAMS syndrome is the presence of a median mandibular cleft (MMC). MMC is a rare occurrence and in this syndrome, it poses a complex challenge for both functional and aesthetic reasons. Patient.

Findings: This rare case report describes the successful correction of an MMC in an 18-month-old child diagnosed with SAMS syndrome.

Treatment: This report describes the presentation, diagnosis and treatment. The surgical intervention involved a meticulous, single stage, osseous reconstruction. The mechanism of MMC in SAMS syndrome is discussed.

Outcomes: Early intervention for MMC in SAMS syndrome patients can offer promising outcomes.

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Source
http://dx.doi.org/10.4103/ijdr.ijdr_461_23DOI Listing

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