AI Article Synopsis
- Pancreatic hamartoma is a rare, benign tumor usually identified through pathology after surgery, characterized by an extremely low incidence.
- A 57-year-old woman was referred for a pancreatic mass and discovered to have an adrenal incidentaloma, with imaging suggesting a pancreatic neuroendocrine tumor and an aldosterone-producing adrenal tumor.
- After a surgery aimed at removing what was thought to be a neuroendocrine tumor, the pathology revealed it was actually a pancreatic hamartoma, raising the possibility of Multiple Endocrine Neoplasia type 1 syndrome explaining her tumors.
Article Abstract
Pancreatic hamartoma is a benign tumor of the pancreas with an extremely low incidence and is commonly diagnosed by pathologic examination after surgery. This report describes the case of a 57-year-old female who was referred for the evaluation of a pancreatic mass and an adrenal incidentaloma. Further imaging studies suggested pancreatic neuroendocrine tumor and aldosterone-producing adrenal tumor. Pylorus-preserving pancreaticoduodenectomy was performed with the initial impression of a pancreatic neuroendocrine tumor. However, pathology results revealed a pancreatic hamartoma. Multiple endocrine neoplasia type 1 syndrome was discussed as a probable explanation for tumor masses in both the pancreas and adrenal gland.
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| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC10444311 | PMC |
| http://dx.doi.org/10.1093/jscr/rjad475 | DOI Listing |
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