ECD is considered to have rapid progression and poor prognosis. Studies have shown that vemurafenib is effective for ECD patients with orbital involvement, but not for ECD with multiple organs. The refinement of treatment approaches and the increased awareness of ECD have led to a dramatic improvement in prognosis.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC10441175PMC
http://dx.doi.org/10.1002/ccr3.7780DOI Listing

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