AI Article Synopsis
- Pediatric transplant recipients with rare genetic kidney diseases require comprehensive, collaborative care among families and a diverse medical team to achieve optimal outcomes.
- This multidisciplinary team includes specialists in various fields, such as surgery, nursing, nutrition, psychology, and more, who work together during preparation, surgery, and follow-up care.
- The review categorizes the genetic renal diseases into five subgroups, highlighting the specific additional care needs for patients beyond standard transplant services.
Article Abstract
In this review, we describe the multidisciplinary, multidimensional care required to optimize outcomes for pediatric transplant recipients with rare genetic kidney diseases. Transplant success, recipient survival, and improvement in quality of life depend on collaboration between patients, families, and a team of specialists with medical, as well as nonmedical expertise. A multidisciplinary transplant team composed of experts from medicine, surgery, nursing, nutrition, social services, transplant coordination, psychology, and pharmacology, is now standard in most transplant centers and is critical to the success of a transplant. In addition to these professionals, other specialists, such as cardiologists, urologists, geneticists, metabolic disease specialists, occupational therapists, case management, child life, chaplain, and palliative care services, have a crucial role to play in the preparation, surgery, and follow-up care, especially when a pediatric patient has a rare genetic disorder leading to renal involvement, and the need for transplantation. In order to describe this multidisciplinary care, we divide the genetic renal diseases into five subgroups-metabolic and tubular disorders, glomerular diseases, congenital anomalies of the kidney and urinary tract, ciliopathies including cystic diseases, and miscellaneous renal conditions; and describe for each, the need for care beyond that provided by the standard transplant team members.
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| http://dx.doi.org/10.1111/petr.14567 | DOI Listing |
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