AI Article Synopsis

  • Hemophilia is an inherited bleeding disorder leading to joint bleeding (hemarthrosis), and this study aims to evaluate the condition of tendons in affected joints of patients with hemophilic arthropathy and suggest eccentric exercise rehabilitation.
  • The study used ultrasound alongside various clinical scales to assess the tendons in 20 patients, finding that while most tendons appeared normal, some showed significant alterations and damage in those with severe joint issues.
  • The findings indicate that tendons in patients with hemophilic arthropathy are negatively impacted by joint disease, but rehabilitation with eccentric exercises is a safe and effective treatment option to enhance tendon properties.

Article Abstract

Background: Hemophilia is a inherited bleeding disorder that is characterized by intra-articular bleeding (hemarthrosis). The aim of the study was to evaluate the state of the satellite tendons of the target joints in the patient with hemophilic arthropathy and propose rehabilitation treatment with eccentric exercises.

Methods: The tendons of the joints mainly affected by hemophilic arthropathy were evaluated by ultrasound. The ultrasound evaluation is associated with the use of evaluation clinical scales, such as the Hemophilia Joint Health Score (HJHS), the Functional Independence Score in Hemophilia (FISH), the Hemophilia Activity List (HAL), the DASH, the VISA-A, the VISA-P, and the VAS scale.

Results: In 20 patients with hemophilic arthropathy, the thickness of the tendons that were examined was normal. In six subjects with severe joint damage, echostructural alterations were present, and signs of hyperemia and neo-vascularization were detected on color Doppler, as well as the presence of intratendinous calcifications.

Conclusions: The tendons of the target joints in patients with hemophilic arthropathy are compromised by the indirect biomechanical damage caused by the joint disease, and rehabilitation treatment with eccentric exercises can be considered safe and effective in improving the tenso-elastic properties of the tendons.

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Source
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC10342756PMC
http://dx.doi.org/10.3390/jcm12134513DOI Listing

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