Total anomalous pulmonary venous connection (TAPVC) is an uncommonly encountered cyanotic congenital heart disease characterized by anomalous drainage of the pulmonary veins. Concomitant venous anomalies are rarely found in these patients. We present a case of an infra-cardiac TAPVC with an intrahepatic portosystemic shunt, where a vascular channel was seen between the middle hepatic vein and the left branch of the portal vein with fusiform dilatation of the latter, diagnosed on computed tomography angiography.
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Risk factors and outcomes for surgical repair of obstructed total anomalous pulmonary venous connection.
Indian J Thorac Cardiovasc Surg
May 2024
Rabindranath Tagore International Institute of Cardiac Sciences, Narayana Health, 124, EM Bypass, Mukundapur, Kolkata, 700099 India.
Article Synopsis
- Surgical repair of obstructed total anomalous pulmonary venous connection (TAPVC) in infants is high-risk, and a study was conducted to evaluate surgical risk factors and outcomes at a single center.
- The study included 41 infants with obstructed TAPVC, revealing a 19.5% in-hospital mortality rate, with significant risk factors being age under 30 days and the need for pre-operative ventilation.
- Follow-up showed reasonable surgical outcomes, with no deaths among the survivors, although some patients developed pulmonary vein obstructions that required additional interventions.
Three-dimensional spatiotemporal imaging correlation in the diagnosis of isolated infracardiac total anomalous pulmonary venous connection in fetal life.
Ann Pediatr Cardiol
September 2023
Tiny Hearts Fetal and Pediatric Cardiac Clinic, Thanjavur, Tamil Nadu, India.
Total anomalous pulmonary venous connection (TAPVC) is a critical congenital heart disease which is often missed on prenatal echocardiography because of the decreased pulmonary blood flow in fetal life. Improvement in technology has resulted in increasing prenatal diagnosis of this condition. We report a foetus with infra cardiac TAPVC in whom prenatal diagnosis was facilitated by the use of STIC technology.
View Article and Find Full Text PDFInfra-cardiac TAPVC with an intrahepatic portosystemic shunt: A rare association.
Ann Pediatr Cardiol
March 2023
Department of Radiodiagnosis and Imaging, Post Graduate Institute of Medical Education and Research, Chandigarh, India.
Total anomalous pulmonary venous connection (TAPVC) is an uncommonly encountered cyanotic congenital heart disease characterized by anomalous drainage of the pulmonary veins. Concomitant venous anomalies are rarely found in these patients. We present a case of an infra-cardiac TAPVC with an intrahepatic portosystemic shunt, where a vascular channel was seen between the middle hepatic vein and the left branch of the portal vein with fusiform dilatation of the latter, diagnosed on computed tomography angiography.
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Pediatr Cardiol
April 2022
Department of Cardiovascular Surgery, Okayama University Graduate School of Medicine, Dentistry and Pharmaceutical Science, Okayama, Japan.
Even today, when the surgical outcome of congenital heart disease in the neonatal period has improved, the prognosis for heterotaxy syndrome and functional single ventricle complicated with total anomalous pulmonary venous connection (TAPVC), especially the infra-cardiac type, is catastrophic. We describe a strategy that combines percutaneous ductus venosus (DV) stent placement and occlusion after TAPVC repair to ensure survival from initial surgery to bidirectional cavopulmonary shunt (BCPS) procedure and facilitate subsequent treatment. Three consecutive patients with heterotaxy syndrome and functional single ventricle complicated by infra-cardiac TAPVC treated with our own strategy were retrospectively studied.
View Article and Find Full Text PDFUnligated vertical vein presenting as a large atrio-portal shunt in adulthood: a case report.
J Surg Case Rep
October 2020
Department of Hepatobiliary and Pancreatic Surgery, Leicester General Hospital, Leicester, UK.
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