Foix-Alajouanine Syndrome: A Case Report.

Cureus

Department of Neurosurgery, Instituto Nacional de Neurología y Neurocirugía Manuel Velasco Suárez, Mexico City, MEX.

Published: March 2023

AI Article Synopsis

  • Foix-Alajouanine syndrome is a rare spinal condition caused by an arteriovenous malformation, leading to myelopathy in the thoracic and lumbar regions.
  • A case study focused on a 46-year-old woman who experienced symptoms like lower limb weakness, sensory loss, back pain, urinary incontinence, and constipation, with imaging revealing abnormal signals from enlarged arteries.
  • Diagnosis can be tricky, often leading to misdiagnosis, but dilated vessels in the posterior epidural space visible on MRIs help in identification; treatments include surgery or endovascular embolization.

Article Abstract

Foix-Alajouanine syndrome is a rare form of presentation of an arteriovenous malformation of the spinal cord that causes myelopathy in the thoracic and lumbar medullary segments. We present the case of a 46-year-old female who suffered from weakness in the lower limbs with sensation loss, low back pain, urinary incontinence, and constipation. The magnetic resonance image T2 sequence of the thoracic spine from T6 to T11 revealed abnormally hypointense signals in the posterior epidural region caused by larger arteries. A spinal digital subtraction angiography was useful to diagnose a right perimedullary fistula with venous drainage, which was satisfactorily embolized. The key to suspecting this diagnosis is the presence of dilated vessels in the posterior epidural space, which are evident in T2 and short tau inversion recovery (STIR)-weighted sequences. Physicians often misdiagnose Foix-Alajouanine syndrome, resulting in potential delays in care. Neurosurgeons can use surgery or endovascular embolization to treat this condition.

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Source
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC10128097PMC
http://dx.doi.org/10.7759/cureus.36696DOI Listing

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