Neuroparalytic keratopathy in Stüve-Wiedemann syndrome treated with tarsoconjunctival flap.

Indian J Ophthalmol

Department of Ophthalmology, Hospital Sant Joan de Deu, Passeig Sant Joan de Déu 2, 08950, Esplugues de Llobregat, Barcelona, Spain.

Published: April 2023

Stüve-Wiedemann syndrome is a rare bone dysplasia with dysautonomic manifestations. Most patients die in the neonatal period or during infancy because of the multiple complications they present. The main ophthalmological complications reported are reduced corneal reflex, corneal anesthesia, hypolacrimation, and severely reduced blinking. We are going to present the first tarsoconjunctival flap in a Stüve-Wiedemann patient, the surgery, and the results in a 13-year-old patient that came to our hospital because of severe corneal ulceration.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC10276720PMC
http://dx.doi.org/10.4103/IJO.IJO_3260_22DOI Listing

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