Fetal permanent junctional reciprocating tachycardia with dilated cardiomyopathy, normal heart rate and transient fetal hydrops; a case report.

J Electrocardiol

Department of Pediatrics, University Hospital Centre Zagreb, Kispaticeva 12, Zagreb, Croatia; University of Zagreb, School of Medicine, Salata 3B, Zagreb, Croatia.

Published: June 2023

AI Article Synopsis

  • PJRT is a rare congenital arrhythmia mainly found in infants and children, often leading to dilated cardiomyopathy (DCM) during pregnancy.
  • Some infants may show a normal heart rate, making diagnosis difficult.
  • In one case, a neonate diagnosed with DCM prenatally had PJRT confirmed after birth, and treatment with digoxin and amiodarone successfully restored normal heart function by 16 months.

Article Abstract

Permanent junctional reciprocating tachycardia (PJRT) is a rare form of congenital arrhythmia occurring predominantly in infants and children. Prenatal presentation is frequently characterized by incessant tachycardia leading to dilated cardiomyopathy (DCM). Some patients can have a normal heart rate which leads to a delayed diagnosis. We report a case of a neonate who was presented prenatally with DCM, fetal hydrops, and no signs of fetal arrhythmia. Diagnosis of PJRT was established after delivery with characteristic electrocardiographic patterns. Successful conversion to sinus rhythm with digoxin and amiodarone was achieved three months later. At 16 months of age, both echocardiography and electrocardiography were normal.

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.jelectrocard.2023.02.005DOI Listing

Publication Analysis

Top Keywords

permanent junctional
8
junctional reciprocating
8
reciprocating tachycardia
8
dilated cardiomyopathy
8
normal heart
8
heart rate
8
fetal hydrops
8
fetal
4
fetal permanent
4
tachycardia dilated
4

Similar Publications

Article Synopsis
  • The study investigated how genetics and environment affect changes in palatal (roof of the mouth) shape during tooth development.
  • Using 3D digital models of dental casts from 228 twin pairs, researchers measured different dimensions of the palate at various dental stages and analyzed the data with genetic modeling techniques.
  • Results showed that while most palatal dimensions increased over time, genetic factors played a significant role, especially in the posterior region, and non-shared environmental factors were also important throughout development.
View Article and Find Full Text PDF

Background: Focal seizures may encompass vestibular sensations in their symptomatology. When these manifestations occur in isolation or constitute the predominant symptom, they prompt consideration for diagnosing recurrent paroxysmal vertigo. However, the characterization of "vestibular epilepsy" remains debated and underexplored.

View Article and Find Full Text PDF

BACKGROUND Cardiac tumors are divided into 2 categories: primary, originating from the heart, and metastatic, which spread to the heart from a different location, with metastatic tumors representing the vast majority. Cardiac tumors, depending on the size and location, can predispose patients to arrhythmic or hemodynamic complications. We present a patient with a history of B-cell lymphoma (DLBCL) in remission for 3 years who developed acute onset congestive heart failure and complete heart block secondary to DLBCL invasion of the myocardium.

View Article and Find Full Text PDF

Isolated abducens nerve palsy (IANP), caused by secondary communicating hydrocephalus, has been rarely documented; in addition, its mechanism and appropriate treatment are not understood well. This study presents a case of bilateral IANP with hydrocephalus in a 62-year-old man who was successfully treated with cerebrospinal fluid (CSF) diversion to correct an enlarged retroclival space during the follow-up of recurrent brain tumor in the right parieto-occipital lobe. The patient was treated with three resections, temozolomide, and irradiation before developing IANP.

View Article and Find Full Text PDF

Despite offering several potential benefits over standard prosthetic aortic valve replacement, the use of the pulmonary autograft has been limited to date due to concerns over the risk of pulmonary autograft expansion and the need for reintervention. Several techniques using materials with biomimetic potential have been developed to reduce this complication. The incidence, risk factors, and pathophysiology of pulmonary autograft dilatation are discussed in this article.

View Article and Find Full Text PDF

Want AI Summaries of new PubMed Abstracts delivered to your In-box?

Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!