AI Article Synopsis
- Bicuspid aortic valve (BAV) is the most common congenital heart condition, and this study aimed to analyze its characteristics in children and teens aged 0-18 using a Spanish registry.* -
- Data was collected from 1681 pediatric patients across 33 hospitals, showing that most were male (69.6%), with 63.7% having isolated BAV and 23.4% having associated left-sided heart conditions.* -
- The findings provide a comprehensive overview of the clinical features and outcomes of BAV in the pediatric population, marking the first large-scale population-based study on this topic in Spain.*
Article Abstract
Introduction And Objectives: Bicuspid aortic valve (BAV) disorder is the most common congenital heart disease. The aim of this study was to describe the characteristics of 0- to 18-year olds with BAV in a population-based registry.
Methods: Data from all pediatric patients were obtained from the Spanish registry for pediatric patients with bicuspid aortic valve (REVAB) (< 18 years). For data analysis, patients with BAV were divided into 2 groups by their features: isolated BAV and BAV with associated congenital heart disease.
Results: We included 1681 patients from 33 hospitals. Males accounted for 69.6% (n = 1158). Valve morphology was horizontal in 63.4% (n = 1012) and pure (Sievers type 0) in 28.4% (n=469). Isolated BAV was present in 63.7% (n=1060), and concomitant left-sided obstructive lesions in 23.4% (n=390). Interventions were required in 8.6% (n=145).
Conclusion: These data represent the first large, population-based description of the clinical presentations and outcomes of patients enrolled in the Spanish registry for pediatric patients with bicuspid aortic valve.
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| http://dx.doi.org/10.1016/j.rec.2023.03.004 | DOI Listing |
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