Inflammatory epilepsy (FIRES) and haemophagocytic lymphohistiocytosis (HLH): an adult case.

BMJ Case Rep

The Neurological Intervention & Imaging Service of Western Australia, Sir Charles Gairdner Hospital, Nedlands, Western Australia, Australia.

Published: January 2023

We describe a man in his 30s with haemophagocytic lymphohistiocytosis (HLH), secondary to an upper respiratory tract infection, with subsequent febrile infection-related epilepsy syndrome. He had a prolonged hospital admission, during which he was treated with chemotherapy for HLH and antiepileptic medications for refractory seizures. He was discharged fully dependent to a care facility and died from aspiration pneumonia 11 months later. This case report highlights his management and discusses these conditions' pathophysiology and future management.

Download full-text PDF

Source
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC9890756PMC
http://dx.doi.org/10.1136/bcr-2022-252637DOI Listing

Publication Analysis

Top Keywords

haemophagocytic lymphohistiocytosis
8
lymphohistiocytosis hlh
8
inflammatory epilepsy
4
epilepsy fires
4
fires haemophagocytic
4
hlh adult
4
adult case
4
case describe
4
describe man
4
man 30s
4

Similar Publications

Want AI Summaries of new PubMed Abstracts delivered to your In-box?

Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!