AI Article Synopsis

  • Identification of ocular manifestations in children with sensorineural hearing loss (SNHL) is crucial for improving treatment outcomes and interventions.
  • Regular screening for both hearing and vision issues is necessary to prevent complications related to the co-occurrence of these conditions.
  • The article reviews various diseases and syndromes linked to these symptoms and categorizes ocular pathologies, while also discussing management strategies for affected patients.

Article Abstract

Identification of ocular manifestations in patients with sensorineural hearing loss (SNHL) can have a large impact on the outcome and treatment of pediatric patients. Due to the common co-incidence of ocular manifestations and SNHL in children, both ophthalmologic and hearing loss screening and routine examinations must be conducted to minimize adverse outcomes and worsening of pathology. Early evaluation and diagnosis is imperative for intervention and further development of the patient. Co-incidence requires a thorough evaluation that includes a comprehensive history, examination, and diagnostic testing. In this article, a literature review was conducted to analyze the presentations of various diseases and syndromes, such as Alport Syndrome, Waardenburg Syndrome, Norrie Disease, Usher Disease, Stickler Syndrome, Marfan Syndrome, Congenital Rubella, and Hereditary Optic Neuropathies. We divided the various ocular pathologies into anterior and posterior segment presentations and associated systemic findings for better understanding. Additionally, this review aims to include an update on the management of patients with both ocular and hearing loss manifestations.

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Source
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC9806326PMC
http://dx.doi.org/10.18502/jovr.v17i4.12321DOI Listing

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