An Unusual Case of Parapharyngeal Desmoid Fibromatosis - A Rare Case Report.

J Indian Assoc Pediatr Surg

Department of Otorhinolaryngology, Civil Hospital, Ahmedabad, Gujarat, India.

Published: September 2022

Desmoid fibromatosis (DF) is a rare locally aggressive, connective tissue malignancy developing in musculoaponeurotic tissues with an incidence of 2-4 per million population. We presented a case of a 3-year-old patient with a left parapharyngeal mass, histopathological examination suggesting DF, who underwent complete surgical excision without recurrence or requirement of cardiac resynchronization therapy.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC9757789PMC
http://dx.doi.org/10.4103/jiaps.jiaps_178_21DOI Listing

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