Introduction And Importance: Prune Belly syndrome is a rare congenital condition first reported in 1939. It is a malformative disease associated with high mortality. We report a neonatal case in a regional hospital in Togo.
Presentation Of Case: A 4-month-old male infant was brought to the hospital by his uncle because of a "deformity of the abdomen and absence of testicles". The examination revealed hypoplasia of the abdominal wall associated with bilateral cryptorchidism. Abdominal and urinary tract ultrasound revealed a left pyelocaliceal dilatation and a right megaureter. All these data allowed the diagnosis of Prune Belly syndrome.
Conclusion: Prune Belly syndrome is a rare and complex disease with a high mortality rate.
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| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC9763359 | PMC |
| http://dx.doi.org/10.1016/j.ijscr.2022.107812 | DOI Listing |
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