Background: Partial arhinia is an extremely rare congenital malformation with an unclear pathogenesis. In this condition, the external nasal structures and nasal passages are absent, and it can be associated with somatic anomalies, other craniofacial abnormalities, severe feeding, and airway compromise.

Objective: In this article, we describe a case of a baby born with congenital partial arhinia at Prince Rashid AlHasan Hospital in Irbid, Jordan.

Case Presentation: Her condition was associated with microcephaly, hypotelorism, cleft palate, microphthalmia, and micrognathia. The baby was the result of an unplanned pregnancy; the mother had received a Zoladex implant 2 months before the pregnancy as a treatment for endometriosis.

Conclusion: Congenital partial arhinia could be associated with dangerous life-threatening complications such as feeding and airway compromise. Management of the condition is essential and urgent, including surgical correction as needed by a highly skilled team.

Download full-text PDF

Source
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC9559655PMC
http://dx.doi.org/10.5455/msm.2022.34.225-227DOI Listing

Publication Analysis

Top Keywords

partial arhinia
16
congenital partial
12
feeding airway
8
congenital
4
arhinia
4
arhinia background
4
background partial
4
arhinia extremely
4
extremely rare
4
rare congenital
4

Similar Publications

Want AI Summaries of new PubMed Abstracts delivered to your In-box?

Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!