AI Article Synopsis
- MNTI is a rare, benign tumor often found in infants, mainly affecting the maxilla, and originates from neural crest cells, but can behave aggressively and mimic cancer.
- A two-year-old girl with a growing upper lip swelling underwent successful tumor resection, and histological tests confirmed it as MNTI.
- Post-surgery, she healed well without recurrence, highlighting that early diagnosis and conservative treatment lead to positive outcomes for MNTI.
Article Abstract
Rationale: Melanotic neuroectodermal tumour of infancy (MNTI) is universally described as a rare, benign, pigmented lesion which most frequently involves the maxilla. Its origin is well established to be in the neural crest cells. Due to the high recurrence rate and aggressive behaviour mimicking malignancy, it poses a great challenge in their diagnosis, treatment planning, and prognosis.
Patient Concern: Two-year-old female with no known comorbidities was brought in with the chief complaint of a growing swelling in the upper lip region.
Diagnosis And Treatment: She was taken up for resection of the tumour under general anaesthesia. The specimen was subjected to histological and immunological examination confirming the diagnosis of MNTI.
Outcome: The postoperative period was uneventful. After regular follow-up, the patient showed satisfactory healing with no signs of recurrence.
Take-away Lessons: Based on our experience, we feel that the diagnosis of MNTI is mainly clinical. Early conservative surgical excision and regular follow-up provide an excellent result with good prognosis.
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| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC9527851 | PMC |
| http://dx.doi.org/10.4103/ams.ams_5_22 | DOI Listing |
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