AI Article Synopsis
- - Pseudoxanthoma elasticum (PXE) is a rare genetic disorder that affects elastic tissue in skin, eyes, and the cardiovascular system, leading to serious complications like gastrointestinal bleeding and fundus hemorrhage.
- - The text discusses a rare case of a PXE patient experiencing acute coronary syndrome (ACS), who is at a high risk for bleeding.
- - It emphasizes the importance of considering antithrombotic therapy as a preventative measure for PXE patients who have developed ACS, due to their heightened bleeding risk.
Article Abstract
Unlabelled: Pseudoxanthoma elasticum (PXE) is a rare hereditary disorder that causes elastic tissue degeneration in the skin, eyes, and cardiovascular system. Gastrointestinal bleeding and fundus hemorrhage are serious complications associated with PXE prognosis as well as cardiovascular involvement. This is a rare case of acute coronary syndrome in a PXE patient with high bleeding risk.
Learning Objective: Pseudoxanthoma elasticum (PXE) resulting in acute coronary syndrome (ACS) is rare. Given PXE patients are generally at very high bleeding risk, antithrombotic therapy as secondary prevention after ACS onset should be taken into full consideration.
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|---|---|
| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC9508624 | PMC |
| http://dx.doi.org/10.1016/j.jccase.2022.06.004 | DOI Listing |
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