AI Article Synopsis
- Langerhans cell histiocytosis is a rare disorder primarily affecting children and young adults, linked to an abnormal increase of Langerhans cells.
- Diagnosing the condition is tricky and usually requires an in-depth pathological examination, despite observable clinical signs and bone lesions.
- The report details a case involving a nine-year-old child with eosinophilic granuloma in the jaw, highlighting its distinct radiological, histopathological, and immunohistochemical characteristics.
Article Abstract
The unusual disorder known as Langerhans cell histiocytosis, which is most frequently seen in children and young adults, is caused by the clonal proliferation of Langerhans cells. Even if clinical signs and radiographic evidence of destructive bone lesions may raise suspicion of the disease, a reliable diagnosis without a thorough pathological examination is challenging. This report describes a case of eosinophilic granuloma of the mandible in a nine-year-old child with characteristic radiological, histopathological, and immunohistochemical features.
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| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC9486456 | PMC |
| http://dx.doi.org/10.7759/cureus.28222 | DOI Listing |
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