Dermatofibrosarcoma is a rare cancer, accounting for 0.01% of all cancers. We here report the case of a 44-year-old female patient presenting with the 5 recurrence of locally advanced Darier-Ferrand dermatofibrosarcoma, that progressed on many cycles of neoadjuvant therapy and required emergency radiotherapy with good response. This allowed to perform wide excision of the tumor with healthy limits. The patient had remission after 1 year of follow-up. Prognosis for patients with Darier-Ferrand dermatofibrosarcoma is generally excellent. Wide surgery and the advent of Mohs surgery have improved local control. The role of radiotherapy is limited for non-resectable tumors or positive margins.
Download full-text PDF |
Source |
|---|---|
| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC9167487 | PMC |
| http://dx.doi.org/10.11604/pamj.2022.41.234.22764 | DOI Listing |
Publication Analysis
Top Keywords
Similar Publications
Darier-Ferrand dermatofibrosarcoma protuberans of the face: Case report and literature review.
Int J Surg Case Rep
July 2024
Pathology and Histology Department, Salah Azaiez Institute of Cancer, Tunis University of Medicine, University Tunis El Manar, Tunis, Tunisia.
Article Synopsis
- - DFSP (Darier Ferrand Dermatofibrosarcoma) is a rare, locally aggressive skin tumor that primarily affects young to middle-aged adults, with about 12.5% of cases occurring in the head and neck region.
- - A specific case involved a 68-year-old patient with DFSP on the lower cheek, treated successfully with surgical removal and reconstruction using a pectoralis major musculocutaneous flap, resulting in a good aesthetic outcome.
- - Effective treatment for DFSP involves complete surgical excision to ensure disease-free survival, emphasizing the importance of early diagnosis, especially for tumors located in the head and neck.
[Fascio-cutaneous exeresis of a dermatofibrosarcoma of Darier-Ferrand of the right flank].
Ann Chir Plast Esthet
January 2024
Service de chirurgie générale A, hôpital central de l'Armée-Dr-Mohamed-Seghir Nekkache, BP 244 Aïn-Naadja, Alger, Kouba, Algérie. Electronic address:
Introduction: Darrier-Ferrand dermatofibrosarcoma (DFSC) is the most common cutaneous sarcoma. It generally affects subjects with an average age of 40 years, without gender or race predominance. It is a tumour characterised by a slow evolution and local aggressiveness.
View Article and Find Full Text PDFDermatofibrosarcoma protuberans of the hallux: A case report with review of the literature.
Int J Surg Case Rep
July 2022
Department of Orthopedic, Homeland Security Forces Hospital La Marsa, United States of America.
Introduction And Importance: Darier-Ferrand dermatofibrosarcoma (DFS) is a rare mesenchymal tumor with an aggressive local behavior, high local recurrence frequency and low metastatic potential. It commonly presents as a raised slowly growing mass. It usually occurs on trunk and proximal extremities but rarely touches distal extremities such as hands, fingers, or foot below knees.
View Article and Find Full Text PDF[Recurrent Darier-Ferrand dermatofibrosarcoma in the abdominal wall: the role of preoperative radiotherapy (case report)].
Pan Afr Med J
June 2022
Service de Radiothérapie, CHU Mohammed VI, Oujda, Maroc.
Dermatofibrosarcoma is a rare cancer, accounting for 0.01% of all cancers. We here report the case of a 44-year-old female patient presenting with the 5 recurrence of locally advanced Darier-Ferrand dermatofibrosarcoma, that progressed on many cycles of neoadjuvant therapy and required emergency radiotherapy with good response.
View Article and Find Full Text PDF[Dermatofibrosarcoma protuberans (Darier-Ferrand) of the abdomen: a case report].
Pan Afr Med J
August 2021
Service de Chirurgie Générale, Sfax, Tunisie.
Dermatofibrosarcoma is a rare skin tumor. Morphological characteristics can be misleading and unknown to most of physicians. Diagnostic delay may affect patient´s management and prognosis.
View Article and Find Full Text PDFWant AI Summaries of new PubMed Abstracts delivered to your In-box?
Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!