AI Article Synopsis
- Eosinophilic granulomatosis with polyangiitis (Churg-Strauss Syndrome) is a rare condition marked by inflammation of small and medium-sized blood vessels, leading to necrotizing vasculitis.
- Symptomatic cardiovascular issues occur in 27% to 47% of cases and are among the most severe complications.
- Early diagnosis, typically via tissue biopsy or cardiac MRI, is crucial for effective treatment and better patient outcomes.
Article Abstract
Eosinophilic granulomatosis with polyangiitis, formerly known as Churg-Strauss Syndrome, is a rare pathology that belongs to the group of diseases characterized by necrotizing vasculitis of small and medium-sized systemic blood vessels. Symptomatic cardiovascular involvement occurs in 27% to 47% of Churg-Strauss cases, being one of the most serious manifestations. The diagnosis is usually confirmed with tissue biopsy showing eosinophil infiltration, but in selected cases with the recent inclusion of cardiac MRI, we can dispense with it. Early diagnosis is important because early treatment is usually associated with improvement in the condition.
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| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC9426326 | PMC |
| http://dx.doi.org/10.31053/1853.0605.v79.n2.32922 | DOI Listing |
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