Febrile infection-related epilepsy syndrome (FIRES) is a disease of unknown etiology, characterized by refractory frequent focal seizures, which require prolonged intensive care. We successfully treated a boy with FIRES with anti-inflammatory and immunosuppressive therapy. This case suggests that an autoimmune mechanism may play a role in the development of FIRES.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC9172588PMC
http://dx.doi.org/10.1002/ccr3.5952DOI Listing

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