Dyke-Davidoff-Masson syndrome (DDMS) is an uncommon neurological disease defined as cerebral hemiatrophy with a contralateral motor deficit, facial asymmetry, and seizures. Classic imaging findings are cerebral hypoplasia, ventriculomegaly, paranasal sinus hyper-pneumatization, and compensatory osseous enlargement. The diagnosis of DDMS is based on the correlation between clinical and neuroimaging features. The management of DDMS is based on anticonvulsant medication with physiotherapy. We describe an unusual case of DDMS presented with frequent and persistent seizures.
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| http://dx.doi.org/10.1016/j.radcr.2022.04.047 | DOI Listing |
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Dyke-Davidoff-Masson syndrome - A dainty spectrum with a diligent diagnosis.
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Department of Family Medicine, Western Michigan University, Homer Stryker MD School of Medicine, Kalamazoo, MI, USA.
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- - Dyke-Davidoff-Masson syndrome is a rare neurological disorder causing severe seizures, brain atrophy on one side (hemiatrophy), and weakness on the opposite side (hemiparesis).
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