AI Article Synopsis
- IgG4-related disease (IgG4-RD) with retroperitoneal fibrosis (RPF) is a rare condition that causes inflammation in the soft tissues of the retroperitoneum.
- A case study of a 73-year-old man showed successful treatment of IgG4-related RPF affecting his abdominal aorta and iliac arteries using steroids and mycophenolate mofetil.
- Early diagnosis is crucial to avoid unnecessary treatments since the disease can be mistaken for other serious conditions and it responds well to steroids.
Article Abstract
Immunoglobulin (Ig)G4-related disease (IgG4-RD) with retroperitoneal fibrosis (RPF) is a rare, fibroinflammatory disease involving the soft tissues of the retroperitoneum. A 73-year-old man with IgG4-related RPF affecting the abdominal aorta and iliac arteries was treated with steroids and mycophenolate mofetil. The prevalence of the disease remains unknown because it is often misdiagnosed and can mimic many malignant, infectious, and inflammatory conditions. Autoimmune pancreatitis is a common presenting condition of IgG4-RD. Because As IgG4-RD is responsive to steroids, diagnosing IgG4-related RPF early can prevent the exposure of patients with RPF to unnecessary diagnostic and therapeutic interventions.
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Source |
|---|---|
| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC9108322 | PMC |
| http://dx.doi.org/10.1016/j.jvscit.2022.02.003 | DOI Listing |
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