AI Article Synopsis
- A 61-year-old male patient experienced anacusis (hearing loss), cerebellar syndrome, myoclonus (muscle jerks), and signs related to frontal lobe dysfunction.
- Brain imaging showed abnormal hyperintensity and restricted diffusion in certain brain areas, indicating possible damage or disease.
- Autopsy findings confirmed Creutzfeldt-Jakob disease, a rare cause of hearing loss, through positive tests for the PrPSc protein.
Article Abstract
We reported a case of a 61-year-old male patient with anacusis, cerebellar syndrome, myoclonus, and frontal signs. The brain magnetic resonance imaging showed bilateral striated hyperintensity of the fluid-attenuated inversion recovery and restricted diffusion in the diffusion-weighted imaging and hypointense areas corresponding to the apparent diffusion coefficient in the cerebral cortex. The autopsy revealed positive immunohistochemistry for the PrPSc protein. Creutzfeldt-Jakob disease presenting with hearing loss is unusual.
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Source |
|---|---|
| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC9018084 | PMC |
| http://dx.doi.org/10.1590/1980-57642021dn15-040016 | DOI Listing |
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