Multiple congenital visceral abnormalities as a rare cause of pulmonary arterial hypertension.

Egypt Heart J

Cardiology and Adult Congenital Heart Disease Department, Rajaei Cardiovascular Medical and Research Center, Iran University of Medical Sciences, Vali-asr Ave, Adjacent to Mellat Park, 1995614331, Tehran, Iran.

Published: April 2022

Background: Pulmonary arterial hypertension (PAH) is a rare, progressive disorder. PAH is caused by a wide spectrum of pathologies but the cause remains undetermined on many occasions and patients are classified in the idiopathic group.

Case Presentation: Here we report a young woman with rare congenital visceral abnormalities presenting with severe pulmonary hypertension.

Conclusions: Pulmonary hypertension is a complex disorder. Search for uncommon conditions that lead to pulmonary hypertension is necessary to determine the best management options.

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Source
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC9050997PMC
http://dx.doi.org/10.1186/s43044-022-00273-xDOI Listing

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