Blue Rubber Bleb Nevus Syndrome is a congenital rarity that manifests as vascular malformations throughout the body, including the gastrointestinal tract. With fewer than 300 cases reported, the etiology and clinical course is poorly understood; however, the literature suggests mutations on chromosome 9 result in unregulated angiogenesis. We present the case of a young female treated for anemia of unknown etiology who presented in hemorrhagic shock due to gastrointestinal hemorrhage necessitating small bowel resection, with cutaneous, intestinal, hepatic, and lingual vascular malformations associated with a single somatic pathologic mutation. Although uncommon, this case suggests that Blue Rubber Bleb Nevus Syndrome should be considered in the differential of a patient with persistent anemia and cutaneous lesions, carrying the potential for multiple gastrointestinal vascular malformations progressing to hemorrhage necessitating operative management. Additionally, a severe phenotype can occur without a double-hit mutation.
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http://dx.doi.org/10.1177/00031348221084949 | DOI Listing |
Langmuir
January 2025
Centre for Nano and Soft Matter Sciences, Shivanapura, Dasanapura Hobli, Bangalore 562162, India.
The textile industry is one of the main industries that benefited from the industrial revolution. Therefore, discharging of dyes from textile, paper, plastic, and rubber industries is inevitable. This colored wastewater prevents sunlight penetration and highly affects water sources.
View Article and Find Full Text PDFPolymers (Basel)
January 2025
Department of Rubber Technology and Polymer Science, Faculty of Science and Technology, Prince of Songkla University, Pattani Campus, Pattani 94000, Thailand.
This study examined the feasibility of using natural rubber (NR) latex foam as a dye adsorbent and antibacterial foam. The dyes used in this experiment were Methylene Blue (MB) and Alizarin Yellow (AY). Foams with that optimum density were further evaluated for adsorption isotherm, kinetics, and thermodynamic data.
View Article and Find Full Text PDFShanghai Kou Qiang Yi Xue
October 2024
Department of Periodontology, School and Hospital of Stomatology, Cheeloo College of Medicine, Shandong University; Shandong Key Laboratory of Oral Tissue Regeneration; Shandong Engineering Research Center of Dental Materials and Oral Tissue Regeneration; Shandong Provincial Clinical Research Center for Oral Diseases. Jinan 250012, Shandong Province, China. E-mail:
Purpose: This study was aimed to compare the difference between iRoot SP and AH Plus on root canal sealing ability for teeth extracted due to severe periodontitis and explore whether the dentin tubule pathway plays an important role in the development of endodontic-periodontic lesions(EPL), in order to provide a theoretical basis for selection of proper time for root canal therapy and suitable root canal sealants in patients with EPL.
Methods: Fifty single-root anterior teeth extracted due to severe periodontitis were selected. The roots were completely debrided to remove the calculus, dental plaque and cementum.
Vasc Specialist Int
December 2024
Department of Vascular Surgery, University General Hospital of Evros, Democritus University of Thrace, Alexandroupolis, Greece.
Inferior vena cava aneurysms (IVCAs) are rare yet potentially lethal, especially if they are symptomatic or complicated. Among the IVCAs reported in the literature, only a few are associated with congenital vascular anomalies, including congenital IVC obstruction, tetralogy of Fallot, left-sided IVC, duplicated IVC, Ehlers-Danlos syndrome, blue rubber bleb nevus syndrome, and Klipper-Trenaunay syndrome. We present the case of an 8-cm symptomatic saccular IVCA in a patient with tetralogy of Fallot, treated successfully with surgical repair.
View Article and Find Full Text PDFSmall
December 2024
Corrosion Laboratory for Light Metals, College of Materials Science and Engineering, Shandong University of Science and Technology, Qingdao, 266590, P. R. China.
Corrosion and degradation of magnesium (Mg) alloy result in serious damage and limit its application in new-energy automobile industry. Considerable protective coating is proposed, yet it is hindered by the difficulties in avoiding and visually monitoring coating micro-damage and localized metal corrosion. Herein, a novel anticorrosion coating system with autonomously monitoring multiple levels of damages in coated Mg-alloy system, is proposed.
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