AI Article Synopsis
- - Atypical teratoid rhabdoid tumor (AT/RT) is a rare type of brain tumor primarily found in young children, constituting 1-2% of pediatric brain tumors and over 10% of CNS tumors in infants, often affecting the cerebellum.
- - The report discusses four new cases of sellar AT/RTs, which were treated using an endoscopic endonasal approach along with various adjuvant therapies.
- - The study aims to highlight the clinical, radiological, and pathological characteristics of these tumors, emphasizing the importance of early diagnosis and effective treatment options.
Article Abstract
Atypical teratoid rhabdoid tumor is a rare lesion that occurs mainly in children can be supratentorial or infratentorial and it accounts for 1-2% of pediatric brain tumors and over 10% of central nervous system (CNS) tumors in infants, with a male preponderance up to 3 years of age, more than 50% of these occur in the cerebellum. In this report we describe four new cases of sellar AT/RTs underwent endoscopic endonasal approach and different adjuvant therapies. Our aim is to report the clinical, radiological and pathological features of these rare lesions, focusing on the possibility to perform an early diagnosis and appropriate therapeutic strategy.
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| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC9010824 | PMC |
| http://dx.doi.org/10.3389/fonc.2022.854437 | DOI Listing |
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