Porokeratotic adnexal ostial nevus (PAON) is a term encompassing porokeratotic eccrine ostial and dermal duct naevus (PEODDN) and porokeratotic eccrine and hair follicle naevus (PEHFN). We present the case of a 7-year-old girl who presented with hyperkeratotic verrucous papules in a blaschkolinear distribution on the sole of her left foot.
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| http://dx.doi.org/10.1002/ccr3.5728 | DOI Listing |
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Mosaic GJB2 mutations in widespread porokeratotic adnexal ostial nevus: Report of two patients.
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Porokeratotic adnexal ostial nevus (PAON) is a rare adnexal hamartoma characterized by keratotic papules following Blaschko's lines, typically located on the unilateral distal extremities. Cutaneous somatic GJB2 mutations have been linked to the pathogenesis of PAON. However, the genetic mechanism underlying bilateral or extended forms, which are less documented, remains unknown.
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- The article discusses a case study of a 6-year-old girl who was diagnosed with this condition, confirmed through a histopathologic examination.
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Porokeratotic adnexal ostial nevus (PAON) is a term encompassing porokeratotic eccrine ostial and dermal duct naevus (PEODDN) and porokeratotic eccrine and hair follicle naevus (PEHFN). We present the case of a 7-year-old girl who presented with hyperkeratotic verrucous papules in a blaschkolinear distribution on the sole of her left foot.
View Article and Find Full Text PDFPorokeratotic adnexal ostial nevus may be misdiagnosed as wart based on clinical appearance and morphology. An accurate diagnosis through skin biopsy is crucial, as is the inclusion of rare disorders such as porokeratotic adnexal ostial nevus in the differential diagnosis.
View Article and Find Full Text PDFLinear porokeratosis with bone abnormalities treated with compounded topical 2% cholesterol/2% lovastatin ointment.
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Department of Dermatology, University of Utah, Salt Lake City, UT, USA.
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