AI Article Synopsis
- - The text discusses Crouzon's syndrome and sinus pericranii (SP), highlighting their rarity and the limited number of cases where both conditions coexist, particularly noting how SP usually drains into the superior sagittal sinus.
- - A specific case is presented where a patient with Crouzon's syndrome has SP located suboccipitally, with the left transverse sinus draining into the SP through cervical venous plexi, while other related sinuses are absent.
- - The conclusion emphasizes that combining Crouzon's syndrome and SP is extremely rare, especially when there’s a connection to major venous sinuses. Proper preoperative diagnosis is crucial to manage these cases and prevent complications like cerebral venous infarction.
Article Abstract
Introduction: Crouzon's syndrome and sinus pericranii (SP) are rare entities. Only few cases having both the features are reported. SP most commonly drains in relation to superior sagittal sinus and their communication to major posterior dural sinuses is rare.
Case Report: We report a rare case of Crouzon's syndrome with SP at a suboccipital location with termination of left transverse sinus into the SP draining further through the extracranial suboccipital and extravertebral cervical venous plexi into external jugular veins. Distal transverse sinus and sigmoid sinus on the left side were absent.
Conclusion: Crouzon's syndrome with SP is an extremely rare entity. SP with communication to major posterior dural venous sinuses is also rare and mostly associated with multi-suture craniosynostosis. Management depends on the volume of venous blood they are draining. Most of them are dominant type and their occlusion is not feasible. Preoperative diagnosis of a dominant SP is essential for proper surgical planning as it needs to be preserved mandatorily to prevent cerebral venous infarction.
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| http://dx.doi.org/10.1159/000524134 | DOI Listing |
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