AI Article Synopsis
- * CMR is a highly sensitive and specific imaging technique with minimal risks, making it a valuable tool for managing HCM patients and identifying different phenotypic forms of the disease.
- * The review covers HCM features in both adults and children, highlighting unique risk factors for kids, and provides important insights and guidelines for general cardiologists on recommending CMR for HCM evaluation.
Article Abstract
Hypertrophic Cardiomyopathy (HCM) is the most frequent hereditary cardiovascular disease and the leading cause of sudden cardiac death in young individuals. Advancements in CMR imaging have allowed for earlier identification and more accurate prognosis of HCM. Interventions aimed at slowing or stopping the disease's natural course may be developed in the future. CMR has been validated as a technique with high sensitivity and specificity, very few contraindications, a low risk of side effects, and is overall a good tool to be employed in the management of HCM patients. The goal of this review is to evaluate the magnetic resonance features of HCM, starting with distinct phenotypic variants of the disease and progressing to differential diagnoses of athlete's heart, hypertension, and infiltrative cardiomyopathies. HCM in children has its own section in this review, with possible risk factors that are distinct from those in adults; delayed enhancement in children may play a role in risk stratification in HCM. Finally, a number of teaching points for general cardiologists who recommend CMR for patients with HCM will be presented.
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|---|---|
| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC8870875 | PMC |
| http://dx.doi.org/10.3390/diagnostics12020489 | DOI Listing |
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