A rare tumor case in an adult patient with neurofibromatosis: Lumbar ependymoma.

Niger J Clin Pract

Department of Neurosurgery, Fırat University, Elazığ, Turkey.

Published: February 2022

In patients with type 1 neurofibromatosis (NF1), there is an increased susceptibility to tumor development in the central nervous system due to the loss of neurofibromin, an inactivator of the protooncogene Ras. NF1 has a broad clinical spectrum,which includes spinal tumors. Although the most common intramedullary tumor of the spinal cord in adults is ependymoma, few patients with NF1 accompanied by spinal ependymoma have been reported to date, and the localization of the tumors is cervical and thoracic in these cases. In this study, we report the case of a patient with NF1 presenting to our clinic with low back pain and gait disturbance. The patient had an intradural extramedullary ependymoma at the L2-3 vertebra level. This report is the first case of NF1 with spinal ependymoma localized in the lumbar region.

Download full-text PDF

Source
http://dx.doi.org/10.4103/njcp.njcp_79_21DOI Listing

Publication Analysis

Top Keywords

ependymoma patients
8
spinal ependymoma
8
report case
8
ependymoma
5
nf1
5
rare tumor
4
tumor case
4
case adult
4
adult patient
4
patient neurofibromatosis
4

Similar Publications

Background: A 32-year-old male with no previous significant medical history presented to the authors' clinic with a 7-week history of severe low back pain. The patient was evaluated with MRI, which revealed a large intradural spherical enhancing mass behind the L1 vertebral body. He was subsequently treated with a left L1-2 hemilaminectomy and excision of the tumor.

View Article and Find Full Text PDF

Introduction: Symptom burden associated with interference in daily functioning is worse in those with progression or higher-grade glial tumors. This exploratory study aims to identify factors associated with its severity in a diverse cross-sectional cohort of 566 brain tumor patients enrolled in a natural history study (NCT03251989, PI: T.S.

View Article and Find Full Text PDF

MicroRNA dysregulation and target genes in common spinal tumors.

Cancer Genet

April 2025

Department of Physiology, Faculty of Medicine, Hormozgan University of Medical Sciences, Bandar Abbas, Iran; Molecular Medicine Research Center, Health Institute, Hormozgan University of Medical Sciences, Bandar Abbas, Iran. Electronic address:

Spinal tumors, although rare, pose significant challenges in diagnosis and treatment due to their complex biological behavior and the variety of tumor types involved. MicroRNAs (miRNAs), small non-coding RNA molecules, have emerged as critical regulators of gene expression and play dual roles as oncogenes or tumor suppressors, depending on their target genes. This review comprehensively examines the role of miRNAs in the pathogenesis and progression of common spinal tumors, including ependymoma, astrocytoma, meningioma, and metastasis, based on existing studies using both human and in vitro models.

View Article and Find Full Text PDF

Background: A hybrid nerve sheath tumor is a biphasic, benign neoplasm of peripheral nerve sheaths, consisting of combinations of neurofibroma, schwannoma, or perineurioma. These tumors were recognized only recently, in 2013; they commonly occur sporadically but rarely with syndromic associations, such as neurofibromatosis syndrome, Carney complex, and schwannomatosis. With an occurrence of 1 in every 33,000 individuals, neurofibromatosis type 2 is a rare autosomal dominant condition characterized by bilateral vestibular schwannomas.

View Article and Find Full Text PDF

Purpose: We characterized the association between photon radiation dose (< 59.4 versus ≥ 59.4 Gy) and outcomes in intracranial ependymoma.

View Article and Find Full Text PDF

Want AI Summaries of new PubMed Abstracts delivered to your In-box?

Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!