AI Article Synopsis
- * This report focuses on two cousins with DBS who underwent cochlear implants to manage their hearing loss, analyzing their progress in auditory and speech skills post-implantation.
- * Results indicated that both patients made significant improvements in hearing, speech perception, and overall intelligence, enabling them to attend mainstream schools, suggesting cochlear implants are a beneficial treatment option for DBS-related hearing loss.
Article Abstract
Donnai-Barrow syndrome (DBS) is a rare autosomal recessive hereditary disorder that affects a variety of body systems. One of the most common symptoms in DBS patients is severe bilateral sensorineural hearing loss. The objective of this report is to highlight the performance of such patients after receiving cochlear implants as a management of their hearing loss. We reviewed the medical records of two cousins diagnosed with DBS before and after cochlear implantation, with a particular focus on their auditory and language performance. After receiving the cochlear implant, both patients showed substantial progress in auditory and speech perception, as well as their intelligence quotients, allowing them to join mainstream schools. In conclusion, our findings showed that cochlear implantation can be considered an ideal approach for the management of DBS patients who suffer from bilateral sensorineural hearing loss.
Download full-text PDF |
Source |
|---|---|
| http://www.ncbi.nlm.nih.gov/pmc/articles/PMC8826483 | PMC |
| http://dx.doi.org/10.7759/cureus.21063 | DOI Listing |
Publication Analysis
Top Keywords
Similar Publications
Assessing the Impact of Vaccination Status on Meningitis Risk Post Cochlear Implantation.
Otolaryngol Head Neck Surg
January 2025
Department of Otolaryngology-Head and Neck Surgery, University Hospitals Cleveland Medical Center/Case Western Reserve School of Medicine, Cleveland, Ohio, USA.
Objective: To better understand the protective benefit of pneumococcal vaccines on rates of meningitis after cochlear implantation.
Study Design: Retrospective large database review.
Setting: Several studies have shown that cochlear implantation increases the incidence of bacterial meningitis, mostly due to pneumococcal meningitis.
Evaluating round window niche visibility in cochlear implantation: anatomical insights and electrode insertion strategies.
Eur Arch Otorhinolaryngol
January 2025
Department of Radiology, Istanbul Training and Research Hospital, University of Health Sciences, Istanbul, Turkey.
Purpose: Cochlear implantation (CI) surgery is essential for restoring hearing in individuals with severe sensorineural hearing loss. Accurate placement of the electrode within the cochlea is essential for successful auditory outcomes and minimizing complications. This study aims to analyze the relationship between the round window niche (RWN) alignment, its visibility during surgery, and the impact on surgical techniques and outcomes.
View Article and Find Full Text PDFExperts' discussion: implications of the World Health Organization's World report on hearing for the cochlear implant field.
Braz J Otorhinolaryngol
January 2025
World Health Organization, Department of Noncommunicable Diseases, Rehabilitation and Disability, Disability and Rehabilitation Unit, Geneva, Switzerland.
Objective: This review aims to analyse the implications of the World Health Organization's 2021 world report on hearing, with a particular focus on the cochlear implant field. The objective is to understand the challenges and opportunities highlighted in the report and propose viable solutions for effective implementation within the cochlear implant community.
Methods: Following the release of the World Health Organization's world report on hearing, cochlear implant professionals explored and discussed the implications of the report with examples from various countries to understand the disparities in access, reimbursement policies, and social stigma associated with hearing loss.
Exploring the relationship between electrophysiological measures of the electrically evoked auditory brainstem response and speech perception outcomes post-cochlear implantation.
Eur Arch Otorhinolaryngol
January 2025
Department of Otolaryngology, China-Japan Friendship Hospital, Beijing, China.
Objectives: This study examined the relationships between electrophysiological measures of the electrically evoked auditory brainstem response (EABR) with speech perception measured in quiet after cochlear implantation (CI) to identify the ability of EABR to predict postoperative CI outcomes.
Methods: Thirty-four patients with congenital prelingual hearing loss, implanted with the same manufacturer's CI, were recruited. In each participant, the EABR was evoked at apical, middle, and basal electrode locations.
Background: Cochlear implantation is an effective method of auditory rehabilitation. Nevertheless, the results show individual variations depending on several factors.
Aim: To evaluate cochlear implantation results based on the APCEI profile (Acceptance, Perception, Comprehension, Oral Expression and Intelligibility) and audiometric results.
Want AI Summaries of new PubMed Abstracts delivered to your In-box?
Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!