Inflammatory myofibroblastic tumor (IMT) is a rare neoplasm of children and young adults. It consists of myofibroblastic cells of borderline malignancy admixed with inflammatory cells. According to the WHO classification, of tumors, it is a soft-tissue tumor with an intermediate malignant potential. It may arise within numerous organs. Ureteral location is exceedingly rare. We report the exceptional case of a 4-year-old boy presenting with a giant right ureteral IMT removed during a nephroureterectomy. Histology and immunohistochemistry confirmed the diagnosis of an IMT with Anaplastic Lymphoma Kinase 1 expression. A 7 months follow-up showed no recurrence or distant metastasis. We also reviewed the literature for similar cases of pediatric ureteral IMT.

Download full-text PDF

Source
http://dx.doi.org/10.1016/j.urology.2022.01.028DOI Listing

Publication Analysis

Top Keywords

giant ureteral
8
inflammatory myofibroblastic
8
myofibroblastic tumor
8
ureteral imt
8
ureteral inflammatory
4
tumor 4-year-old
4
4-year-old child
4
child case
4
case report
4
report review
4

Similar Publications

Broad ligament leiomyomas are rare tumors present outside the uterine body. The incidence of giant broad ligament leiomyomas (weighing over 3 kg) remains relatively rare. In this report, we present the case of a peri-menopausal woman who came in with a large abdominal mass.

View Article and Find Full Text PDF

Prostate sarcoma is extremely rare, comprising less than 0.1 % of prostate cancers. A 61-year-old male presented to the emergency department with urinary retention and hematuria.

View Article and Find Full Text PDF

Neglected double-J stent presenting as giant bladder and ureteral stone: A case report.

Radiol Case Rep

November 2024

Department of Urology, Dr. Soetomo Hospital, Faculty of Medicine, Airlangga University, Surabaya, Indonesia.

Implementing double-J (DJ) stents in urological practice helps to alleviate kidney and ureteral obstruction. The primary causes of neglecting a DJ stent typically involve inadequate counseling and poor patient compliance. Encrustations of neglected DJ stents present a significant challenge.

View Article and Find Full Text PDF
Article Synopsis
  • Retroperitoneal liposarcoma (RPLPS) is a rare and challenging cancer, especially when it's larger than 30 cm, which complicates diagnosis and treatment.
  • A 58-year-old male was diagnosed with a giant RPLPS measuring 55 cm, which had invaded surrounding organs; he underwent successful surgical resection and was discharged with no recurrence after 6 months.
  • Surgery is the most effective treatment for RPLPS, emphasizing the importance of detailed preoperative evaluations, while the necessity of additional therapies like radiotherapy or chemotherapy remains debated.
View Article and Find Full Text PDF

Management of multiple giant bladder diverticula: a comprehensive approach - a case report.

Ann Med Surg (Lond)

July 2024

Department of Urology, Faculty of Medicine, University of Sousse, Ibn El Jazzar Hospital, Kairouan, Tunisia.

Introduction And Importance: Bladder diverticula are commonly due to obstruction of the bladder outlet and are typically treated conservatively. However, the rarity and complexity of multiple giant diverticula require a tailor-made surgical approach.

Case Presentation: We report on a 72-year-old male who presented with severe urinary symptoms and lumbar pain, diagnosed with multiple giant bladder diverticula, including one compressing the ureter.

View Article and Find Full Text PDF

Want AI Summaries of new PubMed Abstracts delivered to your In-box?

Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!