Dystonia is a movement disorder characterised by sustained muscle contractions that produce repetitive twisting movements or abnormal postures. It can be classified according to the aetiology as primary (idiopathic and genetic forms), or secondary. The presentation associated with generalised, intense episodes and with exacerbation of severe muscle contractures and usually refractory to traditional pharmacotherapy is known as dystonic status or dystonic storm. In the present article, a case is presented of a 33-year-old patient with a history of congenital deafness, stimulant use disorder and on psychopharmacological treatment with antipsychotics, who presented with a severe dystonic reaction that evolved to a status dystonicus.
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http://dx.doi.org/10.1016/j.rcpeng.2020.06.001 | DOI Listing |
Neurol India
November 2023
Department of Neurosurgery, Army Hospital (R&R), New Delhi, India.
Ann Indian Acad Neurol
June 2023
Radiodiagnosis, Christian Medical College, Vellore, Tamil Nadu, India.
Background: Status dystonicus (SD) is a life-threatening movement disorder emergency characterized by increasingly frequent and severe episodes of generalized dystonia, requiring urgent hospital admission. The diverse clinico-etiological spectrum, high risk of recurrence, and residual disabilities complicate functional outcomes.
Aim: We aim to describe the clinico-etiological spectrum, radiology, therapeutic options, and follow-up of patients with pre-status dystonicus (pre-SD) and SD.
Parkinsonism Relat Disord
July 2023
Department of Paediatrics (Neurology), University of Galway, Ireland.
Background: Status Dystonicus (SD) represents the most severe end of the spectrum of dystonia. We aimed to explore whether reported features of cases of SD have changed over time.
Methods: A systematic review of cases of SD reported from 2017 to 2023 and comparison of features to data extracted from 2 previous literature reviews (epochs 2012-2017 and pre-2012).
Am J Trop Med Hyg
May 2023
Department of Neurology, King George's Medical University Uttar Pradesh, Lucknow, India.
Subacute sclerosing panencephalitis (SSPE) is a relentlessly progressive brain disorder with invariable mortality. Subacute sclerosing panencephalitis is common in measles-endemic areas. We report an unusual SSPE patient with distinctive clinical and neuroimaging features.
View Article and Find Full Text PDFZh Nevrol Psikhiatr Im S S Korsakova
February 2023
Pirogov Russian National Research Medical University, Moscow, Russia.
Objective: To study the clinical picture of all patients with GNAO1 encephalopathy detected in the Russian Federation. This publication is a multicenter study combining data from epileptological centers in Moscow, Novosibirsk, St. Petersburg, Nizhny Novgorod, Tyumen.
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