[Subtotal sternal agenesis with ectopia cordis: surgical management and long-term outcome (a case in Benin)].

Pan Afr Med J

Département de Chirurgie Pédiatrique de l´Hôpital Mère-Enfant de Las Palmas de Gran Canaria, Unité de Coopération Internationale des Iles Canaries c/ Gran Canaria 7-4°C, 35008 Las Palmas de Gran Canaria, Espagne.

Published: October 2021

Sternal agenesis as well as ectopia cordis are extremely rare congenital malformations. We here report a single case treated in the Department of Paediatric Surgery in Benin. The study involved a 3-year-old girl with congenital sternal agenesis associated with ectopia cordis; firstly, she underwent controlled healing. Then thoracoplasty was performed with favourable outcome. Long-term results are good. Now, she is 13 years old, is attending school and has a satisfactory clinical condition. This is one of the few cases reported in the literature. Optimal therapeutic management has been keeping the patient alive in West Africa.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC8498673PMC
http://dx.doi.org/10.11604/pamj.2021.39.233.25646DOI Listing

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