This is a case report of a female patient with multiple hepatocellular adenomas secondary to the glycogen storage disease 1a with asymptomatic and late adult-onset presentation. Even though the patient was taking a hormonal oral contraceptive, it was important to identify the genetic disorder and ensure adequate metabolic control which is considered a modifier of the adenoma formation and progression. It is also imperative that the patient gets monitored for the adenoma-to-hepatocellular carcinoma transformation.
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Article Synopsis
- Hepatocellular adenoma is a rare, benign liver tumor mostly found in young women using hormonal contraceptives, particularly estrogen.
- A 40-year-old woman experienced severe right upper abdominal pain and instability due to a large bleeding adenoma, which was managed with arterial embolization and then surgical resection.
- The case emphasizes the importance of considering hepatocellular adenoma in younger women on birth control who have severe abdominal pain, highlighting the need for awareness and proper management strategies for this condition.
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