Familial multiple basaloid follicular hamartoma.

Dermatol Online J

Department of Dermatology and Venereology, Centro Hospitalar São João, EPE Porto.

Published: June 2021

AI Article Synopsis

  • Basaloid follicular hamartoma (BFH) is a rare, benign skin condition that can resemble basal cell carcinoma, making accurate diagnosis important.
  • Familial multiple BFH (FMBFH) is a hereditary form that often shows up early, causing multiple small, skin-colored bumps on the face, which may not be painful but can affect appearance.
  • Treatment options include surgery and various therapies like cryotherapy and lasers, but there's no established standard; a case study is presented where CO2 laser treatment successfully addressed FMBFH in adulthood.

Article Abstract

Basaloid follicular hamartoma (BFH) is a rare follicular hamartoma of benign nature, which should be part of the differential diagnoses of basal cell carcinoma. Familial multiple BFH (FMBFH) is a hereditary subtype which typically presents early in life with multiple small, skin-colored papules primarily on the central face. Although these lesions are usually asymptomatic, they can be cosmetically disfiguring. Treatment options include surgery, cryotherapy, CO2 laser and imiquimod; no standard of care has been determined. We present a case of FMBFH presenting in adulthood, which was treated with CO2 laser with satisfactory results.

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Source
http://dx.doi.org/10.5070/D327654066DOI Listing

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