Unilateral Nevoid Telangiectasia in a Healthy Man.

Case Rep Dermatol

Department of Dermatology, Hôpital Erasme, Université libre de Bruxelles, Brussels, Belgium.

Published: June 2021

AI Article Synopsis

  • - The case involves a healthy 26-year-old man with telangiectatic macules on his left thorax and arm since childhood, leading to various diagnostic considerations including unilateral nevoid telangiectasia (UNT) and others.
  • - The ultimate diagnosis was confirmed as UNT, which is a rare condition primarily affecting men, presenting either congenitally or acquired, with congenital cases being less common and stable into adulthood.
  • - Treatment options include pulsed-dye lasers and addressing estrogen levels, along with performing thorough exams to rule out serious underlying conditions like liver or thyroid disorders in cases of unilateral telangiectasia.

Article Abstract

We report the case of a healthy 26-year-old man presenting telangiectatic macules on the left thorax and arm since childhood. The main diagnostic hypothesis were unilateral nevoid telangiectasia (UNT), hereditary benign telangiectasia, atrial myxoma, segmental serpiginous angioma, circumscribed neviform angiokeratoma, and nevus vascularis mixtus. The diagnosis retained was UNT characterized by congenital or acquired telangiectasia distributed asymmetrically along the upper extremities, or the third or fourth cervical dermatomes. The congenital form is extremely rare, predominant in men, and persists in adulthood. The acquired form is most frequent, affects preferentially women, usually appears at puberty or during pregnancy and tends to disappear. Estrogen excess triggers the formation of telangiectasia. UNT is rarely associated with liver or thyroid disorder. Pulsed-dye lasers and normalization of estrogen are proposed as therapeutic options. We report a rare diagnosis of UNT in a young man with no other underlying condition. We would like to highlight that in the presence of unilateral telangiectasia, a complete clinical examination must be performed to rule out signs of hyperestrogenism in man, ocular or neurological abnormalities, a blood test to exclude pregnancy, hepatic and thyroid dysfunctions, and ultrasonography in case of suspicion of atrial myxoma.

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Source
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC8299370PMC
http://dx.doi.org/10.1159/000514941DOI Listing

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