Monoclonal gammopathy of undetermined significance (MGUS) may be associated with pathologies with severe neuromuscular manifestations such as sporadic late-onset nemaline myopathy (SLONM). We describe a difficult to diagnose case of SLNOM with marked clinical improvement after achieving gammopathy complete hematologic response.

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http://www.ncbi.nlm.nih.gov/pmc/articles/PMC8283848PMC
http://dx.doi.org/10.1002/ccr3.4471DOI Listing

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