AI Article Synopsis
- - Erdheim-Chester disease (ECD) is a rare type of blood cancer that can affect the nervous system in different ways.
- - The disease can lead to cerebrovascular issues where transformed histiocytes infiltrate the blood vessels in the head and neck region.
- - A new case study describes a patient with confirmed perivascular microangiopathy that resulted in multiple complications, including ischemia, bleeding, mass formations, and swelling.
Article Abstract
Erdheim-Chester disease (ECD) is a rare and elusive hematopoietic malignancy that may involve the nervous system in various ways. Cerebrovascular ECD involves the perivascular infiltration and compromise of any cervicocranial vessel by transformed proliferating histiocytes. Presented is the novel case of a patient with pathologically proven perivascular microangiopathy, manifesting in multifaceted fashion with ischemia, hemorrhage, mass lesions, and edema.
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| http://dx.doi.org/10.1159/000516803 | DOI Listing |
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