Download full-text PDF |
Source |
|---|
Publication Analysis
Top Keywords
Similar Publications
Atypical teratoid/rhabdoid tumors (AT/RTs) of the central nervous system (CNS) are rare and aggressive, typically occurring in early childhood or infancy, with adult cases being extremely rare. These tumors are associated with the inactivation of the integrase interactor 1 (INI1) gene. The prognosis is poor, worsening significantly if metastasis is detected at diagnosis.
View Article and Find Full Text PDFA rare case of atypical teratoid rhabdoid tumor at the sellar region in an adult: Case report and review of literature.
Brain Spine
November 2024
Department of Neurosurgery, General Hospital of Nikaia 'Agios Panteleimon', 18454, Athens, Greece.
Article Synopsis
- Atypical teratoid/rhabdoid tumor (AT/RT) is a rare brain cancer mainly found in children, but can appear in adults, especially in the sellar region of middle-aged women.
- A case study is presented of a 51-year-old woman with AT/RT who had headaches and left ptosis, leading to a diagnosis and treatment that included surgery, radiation, and chemotherapy.
- Despite treatment, the patient developed lung metastases and passed away seven months post-diagnosis, highlighting the need for further awareness of AT/RT in adults, particularly when considering sellar masses.
Mediastinal Teratoma with Nephroblastomatous Elements: Case Report, Literature Review, and Comparison with Maturing Fetal Glomerulogenic Zone/Definitive Zone Ratio and Nephrogenic Rests.
Int J Mol Sci
November 2024
Department of Pathology, Children's Hospital of Eastern Ontario, University of Ottawa, Ottawa, ON K1H 8L1, Canada.
Article Synopsis
- Extrarenal teratoid Wilms' tumor (TWT) is a rare type of cancer with complex histology, making diagnosis challenging; the case discussed involves an 8-year-old girl with a mediastinal mass containing nephroblastomatous elements.
- Surgical resection revealed a mature cystic teratoma mixed with nephroblastoma, and immunohistochemical tests confirmed the diagnosis, leading to a smooth recovery for the patient.
- This case emphasizes the importance of detailed histopathological analysis in distinguishing TWT from other tumors, underlining the necessity for long-term monitoring due to potential recurrence.
Atypical teratoid/rhabdoid tumor (ATRT) is an aggressive, malignant embryonal tumor with dismal long-term survival despite aggressive multimodal therapy. While this tumor typically presents in infancy or early childhood, there are published case reports of adult-onset ATRT. Making prognostic conclusions or therapeutic decisions for this older patient population remains challenging due to the paucity of these reports.
View Article and Find Full Text PDFCongenital teratoma of the oral cavity - the largest personal series of cases.
Oral Maxillofac Surg
November 2024
Hospital de Clínicas, Federal University of Paraná and Assistance Center for Cleft Lip and Palate, Curitiba, Brazil.
Purpose: The objective of this study is to present the largest personal series of oral teratomas already published in English literature and discuss the diagnosis, neonatal management, and surgical treatment of this disorder.
Method: The study included patients treated by the senior author (RSF) between 2004 and 2023. Data were collected regarding prenatal evaluation, perinatal approach, surgical management, evolution, and treatment of secondary deformities.
Want AI Summaries of new PubMed Abstracts delivered to your In-box?
Enter search terms and have AI summaries delivered each week - change queries or unsubscribe any time!